Sacrococcygeal teratoma in a female newborn with clinical features of trisomy 13: a case report from Central Africa

نویسندگان

  • Toni Kasole Lubala
  • Olivier Mukuku
  • Mick Pongombo Shongo
  • Augustin Mulangu Mutombo
  • Nina Lubala
  • Oscar Numbi Luboya
  • Prosper Lukusa-Tshilobo
چکیده

INTRODUCTION The objective of this report is to describe the first patient presenting clinical features of trisomy 13 in association with a sacrococcygeal teratoma. CASE PRESENTATION We present the case of a Congolese female infant born with bilateral cleft lip and palate, hypotelorism, microcephaly, and capillary hemangioma on her face. She presented with a large sacrococcygeal mass (15.0 cm ×12.0 cm ×5.0 cm) with a cystic consistency and a positive transillumination. CONCLUSION This observation suggests that overexpression of certain genes on chromosome 13 may lead to tumor formation from remnant cells of Hensen's node.

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Sacrococcygeal Teratoma associated with Trisomy 13

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عنوان ژورنال:

دوره 8  شماره 

صفحات  -

تاریخ انتشار 2015